Search on: MITOCHONDRIAL TRIFUNCTIONAL PROTEIN 
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Descriptor English:   Mitochondrial Trifunctional Protein 
Descriptor Spanish:   Proteína Trifuncional Mitocondrial 
Descriptor Portuguese:   Proteína Mitocondrial Trifuncional 
Synonyms English:   FA beta-OMC
Mitochondrial Fatty Acid beta-Oxidation Trifunctional Protein
Mitochondrial Long Chain Enoyl CoA Hydratase 3 Hydroxyacyl CoA Dehydrogenase 3 Ketoacyl CoA Thiolase Trifunctional Protein
Mitochondrial Fatty Acid beta Oxidation Trifunctional Protein
Trifunctional Protein, Mitochondrial  
Tree Number:   D08.811.520.241.300.250.249
D08.811.641.765
D08.811.682.047.820.150.707.249
D08.811.913.050.080.249
D12.776.543.602
D12.776.575.765
Definition English:   A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS. 
History Note English:   2014 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   55285 
Unique Identifier:   D063991 

Occurrence in VHL:
 

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